LA00.00

ICD-11 MMS 2026-01

Craniorachischisis

Description

A condition caused by failure of the neural tube to close completely during the antenatal period. This condition is characterised by complete absence of the skull, extensive defects in the vertebrae and skin, and absence of the brain.

Index terms

  • Craniorachischisis
  • Anencephaly with rachischisis

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA00.0Y – Other specified anencephaly
  • LA00.0Z – Anencephaly, unspecified

Foundation entity

Craniorachischisis – http://id.who.int/icd/entity/675690362

Part of: LA00.0: Anencephaly › LA00: Anencephaly or similar anomalies › 20: Developmental anomalies