Anencephaly or similar anomalies

Description

A malformation of the nervous system caused by the failure of neuropore closure. Infants are born with intact spinal cord, cerebellum, and brainstem, but lack formation of neural structures above this level. The skull is only partially formed but the eyes are usually normal.

Exclusions from above levels

http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Child codes

LA00.0 – Anencephaly
LA00.1 – Iniencephaly
LA00.2 – Acephaly
LA00.3 – Amyelencephaly
LA00.Y – Other specified anencephaly or similar anomalies
LA00.Z – Anencephaly or similar anomalies, unspecified

Sibling codes

LA01 – Cephalocele
LA02 – Spina bifida
LA03 – Arnold-Chiari malformation type II
LA04 – Congenital hydrocephalus
LA05 – Cerebral structural developmental anomalies
LA06 – Cerebellar structural developmental anomalies
LA07 – Structural developmental anomalies of the neurenteric canal, spinal cord or vertebral column
LA0Y – Other specified structural developmental anomalies of the nervous system
LA0Z – Structural developmental anomalies of the nervous system, unspecified

Foundation entity

Anencephaly or similar anomalies – http://id.who.int/icd/entity/458634958

Part of: 20: Developmental anomalies