Polymicrogyria

Description

Polymicrogyria (PMG) is a cerebral cortical malformation characterised by excessive cortical folding and by shallow sulci. Microscopic examination reveals abnormal cortical layering. Topographic distribution of PMG is variable, but bilateral symmetrical perisylvian PMG (BPP) is the most frequent form. PMG is manifested by mild intellectual deficit, epilepsy, and pseudobulbar palsy, which causes difficulties with speech learning and feeding. The severity of PMG is highly dependent on the location and size of the affected area.

Index terms

Polymicrogyria
Bilateral polymicrogyria
Bilateral perisylvian polymicrogyria

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Bilateral frontoparietal polymicrogyria
Bilateral parasagittal parieto-occipital polymicrogyria
Bilateral frontal polymicrogyria
Bilateral generalised polymicrogyria
Unilateral polymicrogyria
Unilateral hemispheric polymicrogyria
Unilateral focal polymicrogyria

Exclusions from above levels

LD20.1 – Lissencephaly
LA01 – Encephalocele
http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

LA05.51 – Cortical dysplasia
LA05.5Y – Other specified abnormal neuronal migration
LA05.5Z – Abnormal neuronal migration, unspecified

Foundation entity

Polymicrogyria – http://id.who.int/icd/entity/2081858551

Part of: LA05.5: Abnormal neuronal migration › LA05: Cerebral structural developmental anomalies › 20: Developmental anomalies