LA01

ICD-11 MMS 2026-01

Cephalocele

Description

A condition caused by failure of the skull to correctly close during the antenatal period. This condition is characterised by herniation of the meninges. This condition may present with herniation of brain, or developmental delay. Confirmation is through observation of herniated meninges by imaging.

Index terms

  • Cephalocele
  • Craniocele
  • Cranial meningocele
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  • Encephalocele
  • Cranium bifidum
  • cerebral meningocele
  • encephalomyelocele
  • meningoencephalocele
  • Frontal encephalocele
  • Fronto-ethmoidal encephalocele
  • Nasal encephalocele
  • nasofrontal encephalocele
  • Occipital encephalocele
  • occipital meningocele
  • Parietal encephalocele
  • Basal encephalocele
  • Orbital encephalocele
  • Nasopharyngeal encephalocele
  • Hydroencephalocele
  • cranial hydromeningocele
  • hydroencephalomeningocele

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA00 – Anencephaly or similar anomalies
  • LA02 – Spina bifida
  • LA03 – Arnold-Chiari malformation type II
  • LA04 – Congenital hydrocephalus
  • LA05 – Cerebral structural developmental anomalies
  • LA06 – Cerebellar structural developmental anomalies
  • LA07 – Structural developmental anomalies of the neurenteric canal, spinal cord or vertebral column
  • LA0Y – Other specified structural developmental anomalies of the nervous system
  • LA0Z – Structural developmental anomalies of the nervous system, unspecified

Foundation entity

Cephalocele – http://id.who.int/icd/entity/1520916568

Part of: 20: Developmental anomalies