LA05.61

ICD-11 MMS 2026-01

Schizencephaly

Description

Schizencephaly is a rare congenital cerebral malformation characterised by the presence of linear clefts in one or both hemispheres of the brain, extending from the lateral ventricles to the pial surface of the cortex, and that lead to a variety of neurological symptoms such as epilepsy, motor deficits, and psychomotor retardation.

Index terms

  • Schizencephaly
  • Schizencephalia

Exclusions from above levels

  • LA01 – Encephalocele
  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA05.60 – Porencephaly
  • LA05.62 – Hydranencephaly
  • LA05.6Y – Other specified encephaloclastic disorders
  • LA05.6Z – Encephaloclastic disorders, unspecified

Foundation entity

Schizencephaly – http://id.who.int/icd/entity/1693546163

Part of: LA05.6: Encephaloclastic disorders › LA05: Cerebral structural developmental anomalies › 20: Developmental anomalies