LA11.2

ICD-11 MMS 2026-01

Anterior segment dysgenesis

Description

A condition caused by failure of the anterior structures of the eye to correctly develop during the antenatal period. This condition may present with iris hypoplasia, irregular and misplaced pupils, hazy corneas, or attachments of the iris to the cornea.

Index terms

  • Anterior segment dysgenesis
  • Axenfeld anomaly
  • Axenfeld syndrome
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  • Rieger-Axenfeld anomaly

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA11.0 – Blue sclera
  • LA11.1 – Structural developmental anomalies of cornea
  • LA11.3 – Aniridia
  • LA11.4 – Coloboma of iris
  • LA11.5 – Congenital corneal opacity
  • LA11.6 – Structural disorders of the pupil
  • LA11.Y – Other specified structural developmental anomalies of the anterior segment of eye
  • LA11.Z – Structural developmental anomalies of the anterior segment of eye, unspecified

Foundation entity

Anterior segment dysgenesis – http://id.who.int/icd/entity/1182282997

Allowed postcoordination axes

Part of: LA11: Structural developmental anomalies of the anterior segment of eye › 20: Developmental anomalies