LA11.3

ICD-11 MMS 2026-01

Aniridia

Description

Aniridia is a congenital ocular malformation characterised by the complete or partial absence of the iris. It can be isolated or part of a syndrome (isolated and syndromic aniridia).

Index terms

  • Aniridia
  • Absence of iris
  • absent iris
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  • agenesis of iris
  • aplasia of iris
  • congenital absence of iris
  • congenital aniridia
  • hereditary aniridia
  • irideremia
  • sporadic aniridia
  • Aniridia, unilateral
  • Aniridia, bilateral

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA11.0 – Blue sclera
  • LA11.1 – Structural developmental anomalies of cornea
  • LA11.2 – Anterior segment dysgenesis
  • LA11.4 – Coloboma of iris
  • LA11.5 – Congenital corneal opacity
  • LA11.6 – Structural disorders of the pupil
  • LA11.Y – Other specified structural developmental anomalies of the anterior segment of eye
  • LA11.Z – Structural developmental anomalies of the anterior segment of eye, unspecified

Foundation entity

Aniridia – http://id.who.int/icd/entity/970699895

Allowed postcoordination axes

Part of: LA11: Structural developmental anomalies of the anterior segment of eye › 20: Developmental anomalies