Congenital lobar emphysema

Description

Congenital lobar emphysema is a developmental lung anomaly characterised by over distension of the affected lobe and leading to compression and displacement of adjacent normal lung tissue and mediastinum. In the majority of cases, symptoms appear during the neonatal period or in early childhood. Clinically, children present with signs of respiratory distress, frequently occurring with a lower respiratory tract infection that aggravates air trapping and renders the patient symptomatic.

Index terms

Congenital lobar emphysema
Congenital lobar emphysema, unilateral
Congenital lobar emphysema, bilateral

Exclusions from above levels

http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

LA75.0 – Accessory lobe of lung
LA75.1 – Agenesis of lung
LA75.2 – Congenital hypoplasia of lung
LA75.3 – Congenital hyperplasia of lung
LA75.4 – Congenital pulmonary airway malformations
LA75.6 – Congenital sequestration of lung
LA75.Y – Other specified structural developmental anomalies of lungs
LA75.Z – Structural developmental anomalies of lungs, unspecified

Foundation entity

Congenital lobar emphysema – http://id.who.int/icd/entity/685349915

Allowed postcoordination axes

Part of: LA75: Structural developmental anomalies of lungs › 20: Developmental anomalies