LA75.6

ICD-11 MMS 2026-01

Congenital sequestration of lung

Description

A medical condition wherein a piece of tissue that ultimately develops into lung tissue is not attached to the pulmonary arterial blood supply, as is the case in normally developing lung. As a result, this sequestered tissue is not connected to the normal bronchial airway. With intralobar sequestration, the lung tissue lies within the same visceral pleura as the lobe in which it occurs With extralobar sequestrations, an accessory lung is contained within its own pleura

Index terms

  • Congenital sequestration of lung
  • Congenital pulmonary sequestration
  • Intralobar sequestration of lung
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  • Extralobar sequestration of lung

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA75.0 – Accessory lobe of lung
  • LA75.1 – Agenesis of lung
  • LA75.2 – Congenital hypoplasia of lung
  • LA75.3 – Congenital hyperplasia of lung
  • LA75.4 – Congenital pulmonary airway malformations
  • LA75.5 – Congenital lobar emphysema
  • LA75.Y – Other specified structural developmental anomalies of lungs
  • LA75.Z – Structural developmental anomalies of lungs, unspecified

Foundation entity

Congenital sequestration of lung – http://id.who.int/icd/entity/1833083626

Allowed postcoordination axes

Part of: LA75: Structural developmental anomalies of lungs › 20: Developmental anomalies