LA86.20

ICD-11 MMS 2026-01

Total anomalous pulmonary venous connection

Description

A congenital cardiovascular malformation in which none of the pulmonary veins connect to the morphologically left atrium.

Index terms

Total anomalous pulmonary venous connection
TAPVC - [total anomalous pulmonary venous connection]
total anomalous pulmonary vein connection

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total anomalous pulmonary venous drainage
total anomalous pulmonary venous return
total pulmonary vein connection anomaly
totally anomalous pulmonary venous connection
Total anomalous pulmonary venous connection of the supracardiac type
TAPVC Type I - [total anomalous pulmonary venous connection Type 1]
total anomalous pulmonary venous connection Type 1
Total anomalous pulmonary venous connection of the cardiac type
TAPVC Type 2 - [total anomalous pulmonary venous connection Type 2]
total anomalous pulmonary venous connection Type 2
total anomalous pulmonary venous connection, intracardiac
Total anomalous pulmonary venous connection of the infracardiac type
TAPVC Type 3 - [Total anomalous pulmonary venous connection Type 3]
Total anomalous pulmonary venous connection Type 3
Total anomalous pulmonary venous connection of the mixed type
TAPVC Type 4 - [Total anomalous pulmonary venous connection Type 4]
Total anomalous pulmonary venous connection Type 4

Exclusions from above levels

http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

LA86.21 – Partial anomalous pulmonary venous connection
LA86.22 – Scimitar syndrome
LA86.2Y – Other specified anomalous pulmonary venous connection
LA86.2Z – Anomalous pulmonary venous connection, unspecified

Foundation entity

Total anomalous pulmonary venous connection – http://id.who.int/icd/entity/1532925990

Part of: LA86.2: Anomalous pulmonary venous connection › LA86: Congenital anomaly of mediastinal vein › 20: Developmental anomalies