LA86.21

ICD-11 MMS 2026-01

Partial anomalous pulmonary venous connection

Description

A congenital cardiovascular malformation in which one or more (but not all) of the pulmonary veins connect anomalously to the right atrium or to one or more of its venous tributaries and the remaining pulmonary veins connect to the left atrium.

Index terms

  • Partial anomalous pulmonary venous connection
  • PAPVC - [partial anomalous pulmonary venous connection]
  • PAPVD - [partial anomalous pulmonary venous drainage]
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  • PAPVR - [partial anomalous pulmonary venous return]
  • partial anomalous pulmonary venous drainage
  • partial anomalous pulmonary venous return
  • partially anomalous pulmonary venous connection

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA86.20 – Total anomalous pulmonary venous connection
  • LA86.22 – Scimitar syndrome
  • LA86.2Y – Other specified anomalous pulmonary venous connection
  • LA86.2Z – Anomalous pulmonary venous connection, unspecified

Foundation entity

Partial anomalous pulmonary venous connection – http://id.who.int/icd/entity/1041585584

Part of: LA86.2: Anomalous pulmonary venous connection › LA86: Congenital anomaly of mediastinal vein › 20: Developmental anomalies