LA88.1

ICD-11 MMS 2026-01

Double chambered right ventricle

Description

A congenital cardiovascular malformation in which the right ventricle is divided into two chambers, one inferior including the inlet and trabecular portions of the right ventricle and one superior including the trabecular portion and infundibulum. Additional information: Double chamber right ventricle is often associated with one or several closing ventricular septal defects. In some cases, the ventricular septal defect is already closed. Double chamber right ventricle is differentiated from the rare isolated infundibular stenosis that develops more superiorly.

Index terms

  • Double chambered right ventricle
  • Anomalous right ventricular muscle bundle
  • DCRV - [double-chambered right ventricle]

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA88.0 – Congenital right ventricular outflow tract obstruction
  • LA88.2 – Tetralogy of Fallot
  • LA88.3 – Congenital left ventricular outflow tract obstruction
  • LA88.4 – Ventricular septal defect
  • LA88.Y – Other specified congenital anomaly of a ventricle or the ventricular septum
  • LA88.Z – Congenital anomaly of a ventricle or the ventricular septum, unspecified

Foundation entity

Double chambered right ventricle – http://id.who.int/icd/entity/997469748

Part of: LA88: Congenital anomaly of a ventricle or the ventricular septum › 20: Developmental anomalies