Tetralogy of Fallot

Description

A group of congenital cardiovascular malformations with biventricular atrioventricular alignments or connections characterised by anterosuperior deviation of the conal or outlet septum or its fibrous remnant, narrowing or atresia of the pulmonary outflow, a ventricular septal defect of the malalignment type, and biventricular origin of the aorta. Additional information: tetralogy of Fallot will always have a ventricular septal defect, narrowing or atresia of the pulmonary outflow, aortic override, and most often right ventricular hypertrophy.

Exclusions from above levels

http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Child codes

LA88.20 – Tetralogy of Fallot with absent pulmonary valve syndrome
LA88.21 – Tetralogy of Fallot with pulmonary atresia
LA88.22 – Tetralogy of Fallot with pulmonary atresia and systemic-to-pulmonary collateral artery
LA88.2Y – Other specified tetralogy of Fallot
LA88.2Z – Tetralogy of Fallot, unspecified

Sibling codes

LA88.0 – Congenital right ventricular outflow tract obstruction
LA88.1 – Double chambered right ventricle
LA88.3 – Congenital left ventricular outflow tract obstruction
LA88.4 – Ventricular septal defect
LA88.Y – Other specified congenital anomaly of a ventricle or the ventricular septum
LA88.Z – Congenital anomaly of a ventricle or the ventricular septum, unspecified

Foundation entity

Tetralogy of Fallot – http://id.who.int/icd/entity/90973426

Part of: LA88: Congenital anomaly of a ventricle or the ventricular septum › 20: Developmental anomalies