LA88.21

ICD-11 MMS 2026-01

Tetralogy of Fallot with pulmonary atresia

Description

A congenital cardiovascular malformation that is a variant of tetralogy of Fallot in which there is no direct communication between the right ventricle and the pulmonary arterial tree.

Index terms

  • Tetralogy of Fallot with pulmonary atresia
  • Pulmonary atresia with ventricular septal defect [Fallot type]

Excludes

  • LA88.22 – Tetralogy of Fallot with pulmonary atresia and systemic-to-pulmonary collateral artery

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA88.20 – Tetralogy of Fallot with absent pulmonary valve syndrome
  • LA88.22 – Tetralogy of Fallot with pulmonary atresia and systemic-to-pulmonary collateral artery
  • LA88.2Y – Other specified tetralogy of Fallot
  • LA88.2Z – Tetralogy of Fallot, unspecified

Foundation entity

Tetralogy of Fallot with pulmonary atresia – http://id.who.int/icd/entity/1645917296

Part of: LA88.2: Tetralogy of Fallot › LA88: Congenital anomaly of a ventricle or the ventricular septum › 20: Developmental anomalies