LA89.0

ICD-11 MMS 2026-01

Double inlet atrioventricular connection

Description

A congenital cardiovascular malformation with a univentricular atrioventricular connection wherein both atria connect to one ventricle either via two separate atrioventricular valves or a common atrioventricular valve, such that all or nearly all of the total atrioventricular junctional (annular) area is committed to one ventricular chamber.

Index terms

  • Double inlet atrioventricular connection
  • DIV - [double inlet ventricle]
  • double inlet ventricle
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  • Double inlet left ventricle
  • Double inlet right ventricle
  • Double inlet to solitary ventricle of indeterminate morphology

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA89.1 – Tricuspid atresia
  • LA89.2 – Mitral atresia
  • LA89.3 – Hypoplastic left heart syndrome
  • LA89.Y – Other specified functionally univentricular heart
  • LA89.Z – Functionally univentricular heart, unspecified

Foundation entity

Double inlet atrioventricular connection – http://id.who.int/icd/entity/1786413029

Part of: LA89: Functionally univentricular heart › 20: Developmental anomalies