LA89.1

ICD-11 MMS 2026-01

Tricuspid atresia

Description

A congenital cardiovascular malformation with absence of the tricuspid valvar annulus (connection/junction) or an imperforate tricuspid valve.

Index terms

  • Tricuspid atresia
  • Tricuspid atresia with absent valvar annulus
  • absent right atrioventricular connection
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  • tricuspid atresia with absent atrioventricular connection
  • tricuspid atresia, absent right atrioventricular connection or junction
  • tricuspid atresia, absent valvar annulus connection or junction
  • Tricuspid atresia with imperforate tricuspid valve

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA89.0 – Double inlet atrioventricular connection
  • LA89.2 – Mitral atresia
  • LA89.3 – Hypoplastic left heart syndrome
  • LA89.Y – Other specified functionally univentricular heart
  • LA89.Z – Functionally univentricular heart, unspecified

Foundation entity

Tricuspid atresia – http://id.who.int/icd/entity/845891723

Part of: LA89: Functionally univentricular heart › 20: Developmental anomalies