Congenital aortic valvar stenosis

Description

A congenital cardiovascular malformation of the aortic valve in which there is narrowing or stricture (obstruction to flow). Additional information: 'Congenital aortic valvar stenosis' arises most commonly as a result of partial or complete fusion of one or more commissures, or is due to dysplasia of one or more aortic cusps. These congenital malformations of the aortic valve may not be initially obstructive but may become stenotic later in life due to leaflet thickening, poor relative growth and-or calcification. It is not until the congenitally malformed aortic valve is or becomes stenotic that this term should be used.

Index terms

Congenital aortic valvar stenosis
Congenital aortic valve stenosis
congenital aortic valve stricture

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congenital stenosis of aortic valve
congenital valvular aortic stenosis

Excludes

LA89.3 – that in hypoplastic left heart syndrome
LA8A.5 – Congenital subaortic stenosis

Exclusions from above levels

LA85.4 – Common arterial trunk
http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

LA8A.21 – Congenital aortic regurgitation
LA8A.22 – Bicuspid aortic valve
LA8A.23 – Aortic valvar atresia
LA8A.24 – Unicuspid aortic valve
LA8A.2Y – Other specified congenital anomaly of aortic valve
LA8A.2Z – Congenital anomaly of aortic valve, unspecified

Foundation entity

Congenital aortic valvar stenosis – http://id.who.int/icd/entity/1824398514

Part of: LA8A.2: Congenital anomaly of aortic valve › LA8A: Congenital anomaly of a ventriculo-arterial valve or adjacent regions › 20: Developmental anomalies