Aortic valvar atresia

Description

A congenital cardiovascular malformation in which there is no orifice of the aortic valve. Additional information: aortic valvar atresia will most often not be coded independently, as it is frequently included within the 'Hypoplastic left heart syndrome' code as part of this spectrum of cardiovascular malformations. However, there is a small subset of patients with aortic valve atresia who have a well developed left ventricle and mitral valve and a large ventricular septal defect (nonrestrictive or restrictive).

Coding note

Aortic valve atresia will most often be coded under the hypoplastic left heart syndrome/complex diagnostic codes since it most often occurs as part of a spectrum of cardiovascular malformations. However, there is a small subset of patients with aortic valve atresia who have a well developed left ventricle and mitral valve and a large ventricular septal defect (nonrestrictive or restrictive).

Index terms

Aortic valvar atresia
aortic valve atresia
aortic valvular atresia

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congenital atresia of aortic valve
imperforate aortic valve

Exclusions from above levels

LA85.4 – Common arterial trunk
http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

LA8A.20 – Congenital aortic valvar stenosis
LA8A.21 – Congenital aortic regurgitation
LA8A.22 – Bicuspid aortic valve
LA8A.24 – Unicuspid aortic valve
LA8A.2Y – Other specified congenital anomaly of aortic valve
LA8A.2Z – Congenital anomaly of aortic valve, unspecified

Foundation entity

Aortic valvar atresia – http://id.who.int/icd/entity/1700740306

Part of: LA8A.2: Congenital anomaly of aortic valve › LA8A: Congenital anomaly of a ventriculo-arterial valve or adjacent regions › 20: Developmental anomalies