LA8B.0

ICD-11 MMS 2026-01

Congenital aortopulmonary window

Description

A congenital cardiovascular malformation in which there is side-to-side continuity of the lumens of the ascending aorta and pulmonary trunk in association with separate aortic and pulmonary valves or their atretic remnants. Additional information: side-to-side continuity of the lumens of the aorta and pulmonary arterial tree, which is distinguished from common arterial trunk (truncus arteriosus) by the presence of two arterial valves or their atretic remnants, and involvement of the pulmonary trunk (main pulmonary artery).

Index terms

  • Congenital aortopulmonary window
  • APW - [aortopulmonary window]
  • Aortic septal defect
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  • Aortopulmonary window
  • aorticopulmonary fenestration
  • aorticopulmonary septal defect
  • aorticopulmonary window
  • aortopulmonary septal defect
  • aortopulmonary septum defect
  • aortopulmonary window

Inclusions

  • Aortic septal defect
  • Aortopulmonary window

Exclusions from above levels

  • LA85.4 – Common arterial trunk
  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA8B.1 – Congenital anomaly of pulmonary arterial tree
  • LA8B.2 – Congenital anomaly of aorta or its branches
  • LA8B.3 – Tracheo-oesophageal compressive syndrome
  • LA8B.4 – Patent arterial duct
  • LA8B.Y – Other specified congenital anomaly of great arteries including arterial duct
  • LA8B.Z – Congenital anomaly of great arteries including arterial duct, unspecified

Foundation entity

Congenital aortopulmonary window – http://id.who.int/icd/entity/1988278118

Part of: LA8B: Congenital anomaly of great arteries including arterial duct › 20: Developmental anomalies