LA8B.1

ICD-11 MMS 2026-01

Congenital anomaly of pulmonary arterial tree

Description

A congenital cardiovascular malformation of the pulmonary trunk (main pulmonary artery) and/or branch pulmonary arteries (right, left, and ramifications).

Index terms

  • Congenital anomaly of pulmonary arterial tree
  • Aberrant pulmonary artery
  • Anomaly of pulmonary artery
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  • Congenital anomalies of pulmonary artery and its branches
  • abnormal origin of pulmonary artery
  • congenital malposition of pulmonary artery
  • pulmonary arterial origin anomaly
  • pulmonary artery abnormality
  • pulmonary artery origin anomaly
  • Congenital dilation of pulmonary arterial tree
  • Congenital pulmonary aneurysm
  • Congenital pulmonary artery aneurysm
  • Idiopathic pulmonary artery dilatation
  • familial pulmonary artery dilatation
  • idiopathic isolated pulmonary arterial dilation
  • Congenital pulmonary trunk anomaly
  • Congenital main pulmonary artery anomaly
  • Congenital pulmonary trunk hypoplasia
  • Main pulmonary artery hypoplasia
  • Absent or atretic pulmonary trunk
  • absent or atretic main pulmonary artery
  • Congenital pulmonary arterial branch anomaly
  • congenital abnormality of pulmonary artery
  • Congenital pulmonary arterial branch stenosis
  • congenital pulmonary artery stricture
  • Congenital right pulmonary arterial stenosis
  • distal peripheral pulmonary stenosis -right
  • peripheral pulmonary stenosis-right
  • Congenital left pulmonary arterial stenosis
  • distal peripheral pulmonary stenosis -left
  • peripheral pulmonary stenosis-left
  • Congenital pulmonary arterial branch hypoplasia
  • congenital hypoplasia of pulmonary artery
  • distal pulmonary artery hypoplasia
  • hypoplasia of pulmonary artery
  • peripheral pulmonary artery hypoplasia
  • pulmonary artery hypoplasia
  • Congenital right pulmonary arterial hypoplasia
  • distal pulmonary artery hypoplasia-right
  • peripheral pulmonary artery hypoplasia-right
  • Congenital left pulmonary arterial hypoplasia
  • distal pulmonary artery hypoplasia-left
  • peripheral pulmonary artery hypoplasia-left
  • Congenital central pulmonary arterial stenosis or hypoplasia proximal to hilar bifurcation
  • Central pulmonary arterial branch stenosis
  • Central pulmonary arterial stenosis
  • Congenital central pulmonary arterial branch stenosis or hypoplasia
  • Proximal pulmonary arterial stenosis
  • Congenital peripheral pulmonary arterial stenosis or hypoplasia at or beyond hilar bifurcation
  • Distal peripheral pulmonary arterial stenosis
  • Distal peripheral pulmonary stenosis
  • Peripheral pulmonary arterial stenosis
  • Peripheral pulmonary stenosis
  • Congenitally discontinuous, non-confluent right and left pulmonary arteries
  • Pulmonary artery origin from ascending aorta
  • hemitruncus
  • Right pulmonary artery from ascending aorta
  • Right hemitruncus
  • Left pulmonary artery from ascending aorta
  • Left hemitruncus
  • Pulmonary artery from arterial duct
  • Pulmonary artery from ductus arteriosus
  • Right pulmonary artery from arterial duct
  • Right pulmonary artery from ductus arteriosus
  • Left pulmonary artery from arterial duct
  • Left pulmonary artery from ductus arteriosus
  • Agenesis of pulmonary artery
  • Absent right or left pulmonary artery
  • Agenesis of branch pulmonary artery
  • Atretic right or left pulmonary artery
  • pulmonary arterial agenesis
  • pulmonary artery absent
  • pulmonary artery agenesis
  • Absent or atretic right pulmonary artery
  • Absent right pulmonary artery
  • Atretic right pulmonary artery
  • Absent or atretic left pulmonary artery
  • Absent left pulmonary artery
  • Atretic left pulmonary artery

Inclusions

  • Aberrant pulmonary artery
  • Anomaly of pulmonary artery

Exclusions from above levels

  • LA85.4 – Common arterial trunk
  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA8B.0 – Congenital aortopulmonary window
  • LA8B.2 – Congenital anomaly of aorta or its branches
  • LA8B.3 – Tracheo-oesophageal compressive syndrome
  • LA8B.4 – Patent arterial duct
  • LA8B.Y – Other specified congenital anomaly of great arteries including arterial duct
  • LA8B.Z – Congenital anomaly of great arteries including arterial duct, unspecified

Foundation entity

Congenital anomaly of pulmonary arterial tree – http://id.who.int/icd/entity/953235173

Allowed postcoordination axes

Part of: LA8B: Congenital anomaly of great arteries including arterial duct › 20: Developmental anomalies