LB21.0ICD-11 MMS 2026-01
Annular pancreas
Description
Annular pancreas is a distinct form of duodenal atresia in which the head of the pancreas forms a ring around the second portion of the duodenum. During the neonatal period, the clinical picture is dominated by epigastric distension with vomiting, which is nonbilious as the obstruction is usually supra-vaterian. Chromosomal abnormalities are present in one-third of cases of annular pancreas, with trisomy 21 (followed by trisomy 18 and 13) being the most frequently detected anomaly. Annular pancreas is an embryopathy resulting from an anomaly occurring early (towards the fourth week) in development.
Index terms
- Annular pancreas
- Pancreas annulare
- congenital annular pancreas
Exclusions from above levels
- http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism
Sibling codes
Foundation entity
Part of: LB21: Structural developmental anomalies of pancreas › 20: Developmental anomalies