LB21.0

ICD-11 MMS 2026-01

Annular pancreas

Description

Annular pancreas is a distinct form of duodenal atresia in which the head of the pancreas forms a ring around the second portion of the duodenum. During the neonatal period, the clinical picture is dominated by epigastric distension with vomiting, which is nonbilious as the obstruction is usually supra-vaterian. Chromosomal abnormalities are present in one-third of cases of annular pancreas, with trisomy 21 (followed by trisomy 18 and 13) being the most frequently detected anomaly. Annular pancreas is an embryopathy resulting from an anomaly occurring early (towards the fourth week) in development.

Index terms

  • Annular pancreas
  • Pancreas annulare
  • congenital annular pancreas

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LB21.1 – Pancreas divisum
  • LB21.2 – Accessory pancreas
  • LB21.3 – Agenesis-aplasia of pancreas
  • LB21.4 – Partial agenesis of pancreas
  • LB21.5 – Hypoplasia of pancreas
  • LB21.Y – Other specified structural developmental anomalies of pancreas
  • LB21.Z – Structural developmental anomalies of pancreas, unspecified

Foundation entity

Annular pancreas – http://id.who.int/icd/entity/1311285827

Part of: LB21: Structural developmental anomalies of pancreas › 20: Developmental anomalies