Partial agenesis of pancreas

Description

Partial agenesis of the pancreas is characterised by the congenital absence of a critical mass of pancreatic tissue. The severity of the disease depends on the amount of functional pancreatic tissue present. Pancreatic agenesis is commonly associated with other malformations, in particular pancreaticobiliary duct anomalies, leading to acute or chronic pancreatitis, hyperglycaemia (50% of cases), or, more rarely, polysplenia.

Index terms

Partial agenesis of pancreas

Exclusions from above levels

http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

LB21.0 – Annular pancreas
LB21.1 – Pancreas divisum
LB21.2 – Accessory pancreas
LB21.3 – Agenesis-aplasia of pancreas
LB21.5 – Hypoplasia of pancreas
LB21.Y – Other specified structural developmental anomalies of pancreas
LB21.Z – Structural developmental anomalies of pancreas, unspecified

Foundation entity

Partial agenesis of pancreas – http://id.who.int/icd/entity/634711891

Part of: LB21: Structural developmental anomalies of pancreas › 20: Developmental anomalies