Arthrogryposis syndromes

Description

Any syndrome caused by failure of elastic tissue to correctly develop during the antenatal period. These syndromes are characterised by the presence of multiple joint contractures, where elastic tissues are replaced by inelastic tissues, which results in fixation of the joint.

Excludes

8C70 – Arthrogryposis due to muscular dystrophy

Exclusions from above levels

http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Child codes

LD26.40 – Multiple pterygium syndrome
LD26.41 – Arthrogryposis multiplex congenita
LD26.4Y – Other specified arthrogryposis syndromes
LD26.4Z – Arthrogryposis syndromes, unspecified

Sibling codes

LD26.0 – Combined reduction defects of upper and lower limbs
LD26.1 – Complex brachydactylies
LD26.2 – Syndromes with limb duplication, polydactyly, syndactyly or triphalangism
LD26.3 – Syndromes with synostoses of limbs
LD26.5 – Constriction rings
LD26.6 – Congenital vascular bone syndromes
LD26.Y – Other specified syndromes with limb anomalies as a major feature
LD26.Z – Syndromes with limb anomalies as a major feature, unspecified

Foundation entity

Arthrogryposis syndromes – http://id.who.int/icd/entity/1692487835

Allowed postcoordination axes

laterality

Part of: LD26: Syndromes with limb anomalies as a major feature › 20: Developmental anomalies