8C70ICD-11 MMS 2026-01
Muscular dystrophy
Description
Progressive, hereditary skeletal muscle diseases characterised by muscle weakness, wasting, defects in muscle proteins, necrosis of muscle tissue and replacement of muscle tissue with connective and fatty tissue.
Exclusions from above levels
Child codes
8C70.0– Becker muscular dystrophy8C70.1– Duchenne muscular dystrophy8C70.2– Emery-Dreifuss muscular dystrophy8C70.3– Facioscapulohumeral muscular dystrophy8C70.4– Limb-girdle muscular dystrophy8C70.5– Scapuloperoneal muscular dystrophy8C70.6– Congenital muscular dystrophy8C70.Y– Other specified muscular dystrophy8C70.Z– Muscular dystrophy, unspecified
Foundation children elsewhere
9C82.1– Muscular dystrophy affecting extraocular muscle
Sibling codes
8C71– Myotonic disorders8C72– Congenital myopathies8C73– Mitochondrial myopathies8C74– Periodic paralyses or disorders of muscle membrane excitability8C75– Distal myopathies8C76– Myofibrillar myopathy8C77– Ocular myopathy8C78– Malignant hyperthermia or hyperpyrexia8C7Y– Other specified primary disorders of muscles8C7Z– Primary disorders of muscles, unspecified
Foundation entity
Muscular dystrophy – http://id.who.int/icd/entity/1464662404
Part of: 08: Diseases of the nervous system