Catalog

Cutaneous mastocytosis

2A21.1

Link to WHO Definition

Cutaneous mastocytosis – http://id.who.int/icd/entity/1300710062

Cutaneous mastocytosis is characterised by abnormal accumulation and proliferation of cutaneous mast cells. Most types are isolated but cutaneous mastocytosis can occur in association with systemic disease. Clinical forms include cutaneous mastocytoma, urticaria pigmentosa (the most frequent form), pseudoxanthomatous nodular cutaneous mastocytosis, telangiectasia macularis eruptiva perstans and diffuse cutaneous mastocytosis.

Parents

Children