Catalog

Papillon-Lefèvre syndrome

No MMS code

Link to WHO Definition

Papillon-Lefèvre syndrome – http://id.who.int/icd/entity/1656270982

Papillon-Lefèvre syndrome (PLS) is a rare autosomal recessive disorder characterised by palmoplantar hyperkeratosis and severe early onset of destructive periodontitis leading to premature loss of both primary and permanent dentitions.