Catalog
Syndromic diffuse palmoplantar keratodermas
No MMS code
Link to WHO Definition
Syndromic diffuse palmoplantar keratodermas – http://id.who.int/icd/entity/2088802678
Diffuse palmoplantar keratoderma associated with extracutaneous abnormalities.
Parents
Children
- Connexin palmoplantar keratoderma with sensorineural deafness
- Odonto-onycho-dermal dysplasia
- Palmoplantar keratoderma with scleroatrophy of the extremities
- Palmoplantar keratoderma – digital clubbing – acro-osteolysis
- Congenital palmoplantar or perioral keratoderma
- Papillon-Lefèvre syndrome
- Cerebral dysgenesis – neuropathy – ichthyosis – keratoderma syndrome
- Autosomal recessive palmoplantar keratoderma and congenital alopecia
- Autosomal dominant palmoplantar keratoderma and congenital alopecia
- LD27.03 Hidrotic ectodermal dysplasia, Clouston type
- Curly hair – acral keratoderma – caries syndrome
- Skin fragility-woolly hair syndrome
- Schöpf-Schulz-Passarge syndrome
- Loricrin palmoplantar keratoderma with ichthyosis