Catalog

Primary ciliary dyskinesia

No MMS code

Link to WHO Definition

Primary ciliary dyskinesia – http://id.who.int/icd/entity/1713839459

Primary ciliary dyskinesia (PCD) is a rare respiratory disease characterised by chronic bronchorrhoea with bronchiectasis and chronic sinusitis. An association with situs inversus occurs in nearly 50% of the cases and constitutes the Kartagener syndrome. PCD is the second most frequent congenital affection of the respiratory tract after cystic fibrosis.

Parents

Children