Catalog
Primary ciliary dyskinesia, Kartagener type
No MMS code
Link to WHO Definition
Primary ciliary dyskinesia, Kartagener type – http://id.who.int/icd/entity/651295257
Primary ciliary dyskinesia, Kartagener type is an autosomal recessive variant of primary cilia dyskinesia which associates respiratory disorders (chronic bronchorrhoea with bronchiectasis and chronic sinusitis) with situs inversus. Men may present with infertility because of immotile sperm.