Catalog
Nodal marginal zone lymphoma
Link to WHO Definition
Nodal marginal zone lymphoma – http://id.who.int/icd/entity/1720785883
A primary nodal B-cell non-Hodgkin lymphoma which morphologically resembles lymph nodes involved by marginal zone lymphomas of extranodal or splenic types, but without evidence of extranodal or splenic disease. This is a rare entity, and most patients present with localised or generalised lymphadenopathy. The clinical course is indolent.