2A85.0

ICD-11 MMS 2026-01

Nodal marginal zone lymphoma

Description

A primary nodal B-cell non-Hodgkin lymphoma which morphologically resembles lymph nodes involved by marginal zone lymphomas of extranodal or splenic types, but without evidence of extranodal or splenic disease. This is a rare entity, and most patients present with localised or generalised lymphadenopathy. The clinical course is indolent.

Index terms

  • Nodal marginal zone lymphoma
  • NMZL - [nodal marginal zone lymphoma]

Exclusions from above levels

  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2A85.1 – Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue of stomach
  • 2A85.2 – Extranodal marginal zone B-cell lymphoma, primary site skin
  • 2A85.3 – Extranodal marginal zone B-cell lymphoma, primary site excluding stomach or skin
  • 2A85.4 – Lymphoplasmacytic lymphoma
  • 2A85.5 – Mantle cell lymphoma
  • 2A85.6 – Burkitt lymphoma including Burkitt leukaemia
  • 2A85.Y – Further specified mature B-cell neoplasms or lymphoma

Foundation entity

Nodal marginal zone lymphoma – http://id.who.int/icd/entity/1720785883

Allowed postcoordination axes

Part of: 2A85: Other specified mature B-cell neoplasms or lymphoma › 02: Neoplasms