Catalog
Pulmonary alveolar proteinosis
Link to WHO Definition
Pulmonary alveolar proteinosis – http://id.who.int/icd/entity/1869739196
This is a rare lung disease in which abnormal accumulation of surfactant occurs within the alveoli, interfering with gas exchange. PAP can occur in a primary form or secondarily in the settings of malignancy (especially in myeloid leukemia), pulmonary infection, or environmental exposure to dusts or chemicals.