Catalog

Autoimmune pulmonary alveolar proteinosis

No MMS code

Link to WHO Definition

Autoimmune pulmonary alveolar proteinosis – http://id.who.int/icd/entity/676409940

Pulmonary alveolar proteinosis (PAP) is a rare restrictive lung disease characterised by the accumulation of a lipoproteinaceous substance in the distal air spaces which stains strongly positive on PAS stain and the PAS diastase stain.