Catalog
Mature T-cell or NK-cell lymphomas and lymphoproliferative disorders, primary cutaneous specified types
No MMS code
Link to WHO Definition
Mature T-cell or NK-cell lymphomas and lymphoproliferative disorders, primary cutaneous specified types – http://id.who.int/icd/entity/1998421548
Primary cutaneous T-cell lymphomas (CTCL) and NK-cell lymphomas are malignant lymphoproliferative diseases of unknown cause that are thought to originate from T-lymphocytes in the lymphoid tissue of the skin and by definition are confined to the skin at initial diagnosis. Included in the class is also a small number of lymphoma-like primary cutaneous lymphoproliferative disorders which are not considered to be truly malignant.
Parents
Children
- 2B03 Primary cutaneous CD30-positive T-cell lymphoproliferative disorders
- Primary cutaneous gamma/delta T-cell lymphoma
- Primary cutaneous aggressive epidermotropic CD8-positive T-cell lymphoma
- Primary cutaneous CD4-positive small or intermediate pleomorphic T-cell lymphoproliferative disorder
- 2B02 Sézary syndrome
- 2B00 Subcutaneous panniculitis-like T-cell lymphoma
- Adult T-cell leukaemia or lymphoma, skin
- Hydroa vacciniforme-like cutaneous T-cell lymphoma
- Primary cutaneous acral CD8-positive T-cell lymphoma
- 2B01 Mycosis fungoides