Catalog

Juvenile polymyositis with interstitial lung disease

No MMS code

Link to WHO Definition

Juvenile polymyositis with interstitial lung disease – http://id.who.int/icd/entity/347167071

Juvenile polymyositis with interstitial lung disease is a rare childhood idiopathic inflammatory myopathy complicated by a serious pulmonary complication commonly seen in patients with polymyositis (PM) and dermatomyositis (DM). The presence of interstitial lung disease affects the prognosis and requires a more aggressive approach in therapy. Patients presenting with fever tend to have a higher frequency of PM/DM-associated interstitial lung disease.