Catalog

Juvenile polymyositis

4A41.10

Link to WHO Definition

Juvenile polymyositis – http://id.who.int/icd/entity/633330307

Juvenile polymyositis is a rare childhood idiopathic inflammatory myopathy. It is frequently misdiagnosed, as it lacks a unique clinical phenotype. Traditionally, it presents with weakness of the proximal muscles that evolves over weeks to months. The primary histologic features are fibre size variability, scattered necrotic and regenerating fibres, and perivascular and endomysial cellular infiltrates.

Parents

Children