Catalog

Combined deficiency of vitamin K-dependent clotting factors

3B14.2

Link to WHO Definition

Combined deficiency of vitamin K-dependent clotting factors – http://id.who.int/icd/entity/54644599

Hereditary combined vitamin K-dependent clotting factors deficiency (VKCFD) is a congenital bleeding disorder resulting from variably decreased levels of coagulation factors II, VII, IX and X, as well as natural anticoagulants protein C, protein S and protein Z.

Parents