Combined deficiency of vitamin K-dependent clotting factors

Description

Hereditary combined vitamin K-dependent clotting factors deficiency (VKCFD) is a congenital bleeding disorder resulting from variably decreased levels of coagulation factors II, VII, IX and X, as well as natural anticoagulants protein C, protein S and protein Z.

Index terms

Combined deficiency of vitamin K-dependent clotting factors
Combined deficiency of factors II,VII,IX and X
Vitamin K epoxide reductase deficiency

Exclusions from above levels

JA43.3 – Postpartum coagulation defects
04 – Diseases of the immune system
05 – Endocrine, nutritional or metabolic diseases

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18 – Complications of pregnancy, childbirth or the puerperium
19 – Certain conditions originating in the perinatal period
20 – Congenital malformations, deformations or chromosomal abnormalities
22 – Injury, poisoning or certain other consequences of external causes
http://id.who.int/icd/entity/1000704511 – Human immunodeficiency virus disease
JB64.1 – Other diseases of the blood or blood-forming organs or certain disorders involving the immune mechanism complicating pregnancy, childbirth or the puerperium

Sibling codes

3B14.0 – Hereditary deficiency of factor I
3B14.1 – Hereditary factor X deficiency
3B14.Z – Other inherited coagulation factor deficiency with bleeding tendency, unspecified

Foundation entity

Combined deficiency of vitamin K-dependent clotting factors – http://id.who.int/icd/entity/54644599

Part of: 3B14: Other inherited coagulation factor deficiency with bleeding tendency › 03: Diseases of the blood or blood-forming organs