Catalog

Paroxysmal nocturnal haemoglobinuria

3A21.0

Link to WHO Definition

Paroxysmal nocturnal haemoglobinuria – http://id.who.int/icd/entity/859588467

Paroxysmal nocturnal hemoglobinuria (PNH) is an acquired clonal hematopoietic stem cell disorder characterised by corpuscular haemolytic anaemia, bone marrow failure and frequent thrombotic events.

Parents