Paroxysmal nocturnal haemoglobinuria

Description

Paroxysmal nocturnal hemoglobinuria (PNH) is an acquired clonal hematopoietic stem cell disorder characterised by corpuscular haemolytic anaemia, bone marrow failure and frequent thrombotic events.

Index terms

Paroxysmal nocturnal haemoglobinuria
Marchiafava-Micheli disease
Marchiafava-Micheli syndrome

Show allHide

nocturnal haemoglobinuria
nocturnal paroxysmal haematuria
nocturnal paroxysmal haemoglobinaemia

Excludes

3A70.1Y – Aplastic anaemia with paroxysmal nocturnal haemoglobulinuria
MF94 – haemoglobinuria NOS

Exclusions from above levels

04 – Diseases of the immune system
05 – Endocrine, nutritional or metabolic diseases
18 – Complications of pregnancy, childbirth or the puerperium

Show allHide

19 – Certain conditions originating in the perinatal period
20 – Congenital malformations, deformations or chromosomal abnormalities
22 – Injury, poisoning or certain other consequences of external causes
http://id.who.int/icd/entity/1000704511 – Human immunodeficiency virus disease
JB64.1 – Other diseases of the blood or blood-forming organs or certain disorders involving the immune mechanism complicating pregnancy, childbirth or the puerperium

Sibling codes

3A21.1 – Microangiopathic haemolytic anaemia
3A21.2 – Haemolytic uraemic syndrome
3A21.Y – Other specified acquired haemolytic anaemia, non-immune
3A21.Z – Acquired haemolytic anaemia, non-immune, unspecified

Foundation entity

Paroxysmal nocturnal haemoglobinuria – http://id.who.int/icd/entity/859588467

Part of: 3A21: Acquired haemolytic anaemia, non-immune › 03: Diseases of the blood or blood-forming organs