Catalog
Demyelination due to systemic vasculitis
Link to WHO Definition
Demyelination due to systemic vasculitis – http://id.who.int/icd/entity/889409107
The CNS vasculature can be targeted by systemic vasculitis and include the following conditions; Small-Medium Vessel Vasculitis - Wegener’s granulomatosis, microscopic polyangiitis, Churg-Strauss syndrome, Cryoglobulinemic vasculitis and Behçet’s disease. Medium Vessel Vasculitis - Polyarteritis nodosa Large Vessel Vasculitis - Giant-cell arteritis, Takayasu’s arteritis (Neurologic complications are mainly due to involvement of extracranial vessels). Usually CNS involvement coexists with other clearly apparent systemic manifestations but some patients may present primarily with prominent symptoms of CNS dysfunction