8A45.44

ICD-11 MMS 2026-01

Demyelination due to systemic vasculitis

Description

The CNS vasculature can be targeted by systemic vasculitis and include the following conditions; Small-Medium Vessel Vasculitis - Wegener’s granulomatosis, microscopic polyangiitis, Churg-Strauss syndrome, Cryoglobulinemic vasculitis and Behçet’s disease. Medium Vessel Vasculitis - Polyarteritis nodosa Large Vessel Vasculitis - Giant-cell arteritis, Takayasu’s arteritis (Neurologic complications are mainly due to involvement of extracranial vessels). Usually CNS involvement coexists with other clearly apparent systemic manifestations but some patients may present primarily with prominent symptoms of CNS dysfunction

Index terms

  • Demyelination due to systemic vasculitis

Exclusions from above levels

  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
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  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • 8A45.40 – Demyelination due to sarcoidosis
  • 8A45.41 – Demyelination due to systemic lupus erythematosus
  • 8A45.42 – Demyelination due to Sjögren disease
  • 8A45.43 – Demyelination due to Behcet disease
  • 8A45.45 – Demyelination due to mitochondrial disease
  • 8A45.4Z – White matter disorders due to certain specified systemic disease, unspecified

Foundation entity

Demyelination due to systemic vasculitis – http://id.who.int/icd/entity/889409107

Allowed postcoordination axes

Part of: 8A45.4: White matter disorders due to certain specified systemic disease › 8A45: Secondary white matter disorders › 08: Diseases of the nervous system