Catalog
Catecholaminergic polymorphic ventricular tachycardia
Link to WHO Definition
Catecholaminergic polymorphic ventricular tachycardia – http://id.who.int/icd/entity/976309888
Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a severe genetic arrhythmogenic disorder of childhood characterised by adrenergically-induced ventricular tachycardia (bidirectional ventricular tachycardia and, less frequently, supraventricular tachycardia and atrial fibrillation) manifesting as syncope and sudden death.