Catalog

Catecholaminergic polymorphic ventricular tachycardia

BC65.5

Link to WHO Definition

Catecholaminergic polymorphic ventricular tachycardia – http://id.who.int/icd/entity/976309888

Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a severe genetic arrhythmogenic disorder of childhood characterised by adrenergically-induced ventricular tachycardia (bidirectional ventricular tachycardia and, less frequently, supraventricular tachycardia and atrial fibrillation) manifesting as syncope and sudden death.

Parents

Children