Catecholaminergic polymorphic ventricular tachycardia

Description

Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a severe genetic arrhythmogenic disorder of childhood characterised by adrenergically-induced ventricular tachycardia (bidirectional ventricular tachycardia and, less frequently, supraventricular tachycardia and atrial fibrillation) manifesting as syncope and sudden death.

Index terms

Catecholaminergic polymorphic ventricular tachycardia
Catecholaminergic polymorphic ventricular tachycardia due to RYR2 mutation
Catecholaminergic polymorphic ventricular tachycardia due to Calsequestrin mutation

Exclusions from above levels

01 – Certain infectious or parasitic diseases
05 – Endocrine, nutritional or metabolic diseases
18 – Complications of pregnancy, childbirth and the puerperium

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19 – Certain conditions originating in the perinatal period
20 – Congenital malformations, deformations and chromosomal abnormalities
22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

BC65.0 – Long QT syndrome
BC65.1 – Brugada syndrome
BC65.2 – Short QT syndrome
BC65.3 – Early repolarisation syndrome
BC65.4 – Idiopathic ventricular fibrillation
BC65.Y – Other specified cardiac arrhythmia associated with genetic disorder
BC65.Z – Cardiac arrhythmia associated with genetic disorder, unspecified

Foundation entity

Catecholaminergic polymorphic ventricular tachycardia – http://id.who.int/icd/entity/976309888

Part of: BC65: Cardiac arrhythmia associated with genetic disorder › 11: Diseases of the circulatory system