1F2E

ICD-11 MMS 2026-01

Paracoccidioidomycosis

Description

A disease caused by an infection with the fungi Paracoccidioides brasiliensis. This disease commonly presents with fever, toxaemia, weight loss, adenopathy, hepatosplenomegaly, anaemia, or eosinophilia. This disease may present with symptoms similar to tuberculosis, leukaemia, or lymphoma. Transmission is by inhalation of fungal spores. Confirmation is by identification of Paracoccidioides brasiliensis in a blood, sputum, or skin sample.

Exclusions from above levels

  • 2B01 – Mycosis fungoides
  • CA70 – Hypersensitivity pneumonitis due to organic dust
  • NE83.1 – Infection arising from device, implant or graft, not elsewhere classified

Child codes

  • 1F2E.0 – Pulmonary paracoccidioidomycosis
  • 1F2E.1 – Disseminated paracoccidioidomycosis
  • 1F2E.Y – Other specified paracoccidioidomycosis
  • 1F2E.Z – Paracoccidioidomycosis, unspecified

Sibling codes

  • 1F20 – Aspergillosis
  • 1F21 – Basidiobolomycosis
  • 1F22 – Blastomycosis
  • 1F23 – Candidosis
  • 1F24 – Chromoblastomycosis
  • 1F25 – Coccidioidomycosis
  • 1F26 – Conidiobolomycosis
  • 1F27 – Cryptococcosis
  • 1F28 – Dermatophytosis
  • 1F29 – Eumycetoma
  • 1F2A – Histoplasmosis
  • 1F2B – Lobomycosis
  • 1F2C – Mucormycosis
  • 1F2D – Non-dermatophyte superficial dermatomycoses
  • 1F2F – Phaeohyphomycosis
  • 1F2G – Pneumocystosis
  • 1F2H – Scedosporiosis
  • 1F2J – Sporotrichosis
  • 1F2K – Talaromycosis
  • 1F2L – Emmonsiosis
  • 1F2Y – Other specified mycoses
  • 1F2Z – Mycoses, unspecified

Foundation entity

Paracoccidioidomycosis – http://id.who.int/icd/entity/268777657

Part of: 01: Certain infectious or parasitic diseases