2A21.00

ICD-11 MMS 2026-01

Mast cell leukaemia

Index terms

  • Mast cell leukaemia
  • mast cell leukaemia NOS
  • mast cell leukaemia without mention of remission
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  • Aleukaemic mast cell leukaemia
  • Classic mast cell leukaemia
  • Mast cell leukaemia in complete remission

Exclusions from above levels

  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2A21.0Y – Other specified systemic mastocytosis
  • 2A21.0Z – Systemic mastocytosis, unspecified

Foundation entity

Mast cell leukaemia – http://id.who.int/icd/entity/1359806843

Allowed postcoordination axes

Part of: 2A21.0: Systemic mastocytosis › 2A21: Mastocytosis › 02: Neoplasms