2A21.0Z

ICD-11 MMS 2026-01

Systemic mastocytosis, unspecified

Exclusions from above levels

  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2A21.00 – Mast cell leukaemia
  • 2A21.0Y – Other specified systemic mastocytosis

Foundation entity

Systemic mastocytosis – http://id.who.int/icd/entity/1144812971

Allowed postcoordination axes

Part of: 2A21.0: Systemic mastocytosis › 2A21: Mastocytosis › 02: Neoplasms