Systemic mastocytosis

Description

Systemic mastocytosis (SM) comprises a heterogeneous group of rare acquired and chronic haematological malignancies that are related to an abnormal proliferation of mast cells in tissue, including bone marrow, with or without skin involvement. SM can be divided into indolent SM (ISM) and aggressive SM (ASM).

Exclusions from above levels

2E03 – Malignant neoplasm metastasis in bone or bone marrow
http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Child codes

2A21.00 – Mast cell leukaemia
2A21.0Y – Other specified systemic mastocytosis
2A21.0Z – Systemic mastocytosis, unspecified

Sibling codes

2A21.1 – Cutaneous mastocytosis
2A21.2 – Mast cell sarcoma
2A21.3 – Extracutaneous mastocytoma
2A21.Y – Other specified mastocytosis
2A21.Z – Mastocytosis, unspecified

Foundation entity

Systemic mastocytosis – http://id.who.int/icd/entity/1144812971

Allowed postcoordination axes

Part of: 2A21: Mastocytosis › 02: Neoplasms