2A21.2

ICD-11 MMS 2026-01

Mast cell sarcoma

Description

A rare entity characterised by localised but destructive growth of a tumour consisting of highly atypical, immature mast cells.

Index terms

  • Mast cell sarcoma

Exclusions from above levels

  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2A21.0 – Systemic mastocytosis
  • 2A21.1 – Cutaneous mastocytosis
  • 2A21.3 – Extracutaneous mastocytoma
  • 2A21.Y – Other specified mastocytosis
  • 2A21.Z – Mastocytosis, unspecified

Foundation entity

Mast cell sarcoma – http://id.who.int/icd/entity/233404891

Allowed postcoordination axes

Part of: 2A21: Mastocytosis › 02: Neoplasms