2A83.1

ICD-11 MMS 2026-01

Plasma cell myeloma

Description

A bone marrow-based plasma cell neoplasm usually characterised by presence of a serum monoclonal protein and/or urinary light chains. ”CRAB” criteria (calcium elevation (hypercalcaemia), renal failure, anaemia and bone lesions) separate symptomatic plasma cell myeloma from asymptomatic (smoldering) myeloma.

Index terms

  • Plasma cell myeloma
  • Kahler disease
  • MM - [multiple myeloma]
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  • Medullary plasmacytoma
  • Myelomatosis
  • monostotic plasma cell myeloma
  • multiple myeloma
  • multiple myeloma NOS
  • multiple myeloma without mention of remission
  • multiple myelomata
  • myeloma
  • plasmacytic myeloma
  • Osteoporosis in multiple myelomatosis
  • Osteoporosis in multiple myelomatosis, multiple sites
  • Osteoporosis in multiple myelomatosis, shoulder region
  • Osteoporosis in multiple myelomatosis, acromioclavicular joints
  • Osteoporosis in multiple myelomatosis, clavicle
  • Osteoporosis in multiple myelomatosis, glenohumeral joints
  • Osteoporosis in multiple myelomatosis, sternoclavicular joints
  • Osteoporosis in multiple myelomatosis, scapula
  • Osteoporosis in multiple myelomatosis, upper arm
  • Osteoporosis in multiple myelomatosis, elbow joint
  • Osteoporosis in multiple myelomatosis, humerus
  • Osteoporosis in multiple myelomatosis, forearm
  • Osteoporosis in multiple myelomatosis, radius
  • Osteoporosis in multiple myelomatosis, ulna
  • Osteoporosis in multiple myelomatosis, wrist joint
  • Osteoporosis in multiple myelomatosis, hand
  • Osteoporosis in multiple myelomatosis, carpus
  • Osteoporosis in multiple myelomatosis, fingers
  • Osteoporosis in multiple myelomatosis, metacarpus
  • Osteoporosis in multiple myelomatosis, pelvic region or thigh
  • Osteoporosis in multiple myelomatosis, femur
  • Osteoporosis in multiple myelomatosis, hip joint
  • Osteoporosis in multiple myelomatosis, pelvis
  • Osteoporosis in multiple myelomatosis, sacroiliac joint
  • Osteoporosis in multiple myelomatosis, lower leg
  • Osteoporosis in multiple myelomatosis, tibia
  • Osteoporosis in multiple myelomatosis, fibula
  • Osteoporosis in multiple myelomatosis, knee joint
  • Osteoporosis in multiple myelomatosis, ankle or foot
  • Osteoporosis in multiple myelomatosis, ankle joint
  • Osteoporosis in multiple myelomatosis, metatarsus
  • Osteoporosis in multiple myelomatosis, other joints in foot
  • Osteoporosis in multiple myelomatosis, tarsus
  • Osteoporosis in multiple myelomatosis, toes
  • Osteoporosis in multiple myelomatosis, head
  • Osteoporosis in multiple myelomatosis, neck
  • Osteoporosis in multiple myelomatosis, ribs
  • Osteoporosis in multiple myelomatosis, skull
  • Osteoporosis in multiple myelomatosis, trunk
  • Osteoporosis in multiple myelomatosis, vertebral column
  • Plasma cell myeloma in complete remission
  • multiple myeloma in complete remission

Inclusions

  • Kahler disease
  • Medullary plasmacytoma
  • Myelomatosis
  • multiple myeloma

Excludes

  • 2A83.2 – Solitary plasmacytoma

Exclusions from above levels

  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2A83.0 – Monoclonal gammopathy of undetermined significance
  • 2A83.2 – Solitary plasmacytoma
  • 2A83.3 – Extraosseous plasmacytoma
  • 2A83.4 – Plasma cell leukaemia
  • 2A83.5 – Monoclonal immunoglobulin deposition disease
  • 2A83.Y – Other specified plasma cell neoplasms
  • 2A83.Z – Plasma cell neoplasm, unspecified

Foundation entity

Plasma cell myeloma – http://id.who.int/icd/entity/526287100

Allowed postcoordination axes

Part of: 2A83: Plasma cell neoplasms › 02: Neoplasms